Sell, who has repaired more than a dozen cases of ALCAPA in children and several in adults, is one of the most experienced surgeons in the world treating the rare and complex heart defect.
Because it is so rare, no long-term studies of adults with corrected ALCAPA are available, but the prognosis is generally good in children, and Drs.
Catheterization-angiography was decided to be performed considering ALCAPA as a result of echocardiographic examination.
14) reported that they false negatively observed the origin of the left coronary artery to be normal in their series of three patients and the origin of the left coronary artery should be demonstrated echocardiographically or angiographic evaluation should be done in patients in whom ALCAPA is suspected (14).
There are two types of ALCAPA
syndrome: the adult and the infant type.
About 10% of ALCAPA
patients can survive to adulthood by well-developed intercoronary and extra coronary systemic collaterals (mainly from the bronchial arteries) (2, 4).
The acronym ALCAPA
stands for 'anomalous left coronary artery originating from the pulmonary artery.
A diagnosis of ALCAPA
syndrome was made as a result of diagnostic angiography and with clinical electrocardiographical and echocardiographical findings in a 28 days old patient with dilated cardiomyopahty (DCM) and congestive cardiac failure.
Her rare condition, known as ALCAPA
, baffled doctors and sparked an emergency five-hour procedure to save her life.