To describe the death and survival of males with DBMD, MD STARnet subjects born during 1983-2002 and who ever resided in the four geographic areas were included in the analysis.
On January 1, 2007, 452 definite or probable cases of DBMD in males born during 1983-2002 were identified in the four states.
Of the 58 deaths, 54 (93%) were attributable to DBMD.
Editorial Note: This report describes the first population-based assessment of DBMD prevalence in the United States.
The case classification used by MD STARnet rigorously defines probable or definite cases, but might not identify all cases of DBMD.
Data show that some males (29%) who have DBMD experience impaired mobility by the end of their first decade of life and more than 90% used wheelchairs by the end of their second decade of life.
As males with DBMD increasingly survive into adulthood, practitioners who care for adults are increasingly challenged to manage patients who have rare disorders, such as DMD, who historically did not survive to adulthood.
Fourth, the variable follow-up period was too brief to observe longterm survival for all males with DBMD.
DBMD results from both familial and new genetic mutations; therefore, any newborn male can be affected.