[ClickPress, Tue Jul 16 2019] By epidemiology, according to the Centers for Diseases Control and Prevention, arrhythmogenic
right ventricular dysplasia has a prevalence of 1 in 2500 to 1 in 5000 population.
Diagnostic and Therapeutic Strategies for Arrhythmogenic
Right Ventricular Dysplasia / Cardiomyopathy Patient.
Noninvasive approaches including computed tomography (CT) and magnetic resonance imaging enable observation of fibrofatty infiltration of the myocardium in healthy subjects and in conditions of cardiomyoptahy, states after myocardial infarction, arrhythmogenic
right ventricular dysplasia, and others (5,14-17).
Arrhythmogenic
right ventricular dysplasia: a United States experience.
Dysplastic conditions of the right ventricular myocardium: Uhl's anomaly vs arrhythmogenic
right ventricular dysplasia. Br Heart J 1993; 69(2):142-150.
Wen et al., "Studying arrhythmogenic
right ventricular dysplasia with patient-specific iPSCs," Nature, vol.
The term arrhythmogenic
right ventricular dysplasia was first used by Frank et al.
This condition must be distinguished from other established clinical entities presenting prominent trabeculations including: apical hyperthrophic cardiomyopathy, dilated cardiomyopathy, arrhythmogenic
right ventricular dysplasia and endocardial fibroelastosis.
For example, in young athletes (younger than 35 years) the vast majority of sudden deaths are due to underlying cardiovascular abnormalities including hypertrophic cardiomyopathy, congenital coronary anomalies and arrhythmogenic
right ventricular dysplasia (ARVD).
For the first time, the report rated cardiac CT as appropriate in patients with suspected arrhythmogenic
right ventricular dysplasia, and as uncertain for evaluation of myocardial viability when other imaging modalities are inadequate or contraindicated.
Cardiomyopathies such as hypertrophic cardiomyopathy, dilated cardiomyopathy and arrhythmogenic
right ventricular dysplasia account for approximately 10-15 per cent of sudden deaths (2).
The screening program was predicated on an unusually high incidence of arrhythmogenic
right ventricular dysplasia (ARVD) in the region, however, and the 89% drop reported in the JAMA study brings the rate of sudden cardiac death in the region "to about what we see in our country," Dr.