(redirected from Endolymphatic Sac Tumor)
ELSTEndolymphatic Sac Tumor (neuroectodermal tumor)
ELSTEast Lake Sammamish Trail (Washington)
ELSTEnglish Language Support Team (UK)
ELSTEnglish Language Study Tours (San Diego, CA)
Copyright 1988-2018 AcronymFinder.com, All rights reserved.
References in periodicals archive ?
Paraganglioma, (52,53) schwannoma, (54) meningioma, (54) and endolymphatic sac tumor (55) may be multifocal/bilateral, raising the possibility of familial or syndromic association, and requiring appropriate clinical investigation or confirmation.
Endolymphatic sac tumor: A report of 3 cases and discussion of management.
Endolymphatic sac tumor (ELST) is a papillary epithelial neoplasm arising within the endolymphatic sac/ duct that shows a high association with von Hippel-Lindau disease (VHL).
The differential diagnostic considerations for a middle ear mass include both benign neoplasms (e.g., adenoma, endolymphatic sac tumor, choristoma, cholesteatoma, cholesterol granuloma) and malignant neoplasms (e.g., squamous cell carcinoma, adenocarcinoma, and sarcoma).
All except 2 cases demonstrated apical petrous temporal bone invasion on imaging, and it has been suggested that they arose from a primary endolymphatic sac tumor, which has a similar papillary epithelial histology.
Patients with an endolymphatic sac tumor (ELST) typically present with palsy of cranial nerves VII and/or VIII; other presenting symptoms include hearing loss, otalgia, occipital headaches, cranial nerve palsies, vertigo, gait ataxia, tinnitus, and otorrhea.
On imaging studies, each patient had a different pathologic lesion that involved the endolymphatic sac or duct: patient 1 had a jugular megabulb, and she was ultimately treated with vestibular nerve section; patient 2 had a cholesterol granuloma, which was treated with surgical excision; patient 3 had an endolymphatic sac tumor that was treated with surgical excision.
The term "secondary hydropic ear disease" describes the conditions that cause hydrops of the inner ear secondarily (such as endolymphatic sac tumors).
They cover otosclerosis surgery; chronic ear disease surgery; canalplasty; cholesterol granuloma; cerebral spinal fluid leaks, encephalocele,or pseudo-meningocele; posterior fossa tumor surgery; glomus tumors; hypoglossal foramen and foreman magnum tumors; endolymphatic sac tumors; carcinoma involving the temporal bone; implantable middle ear devices; cochlear implant surgery; auditory brainstem implant; surgery for Meniere disease; repair of superior semicircular canal dehiscence; surgery for benign positional postural vertigo; facial decompression; and facial nerve repair and facial palsy rehabilitation.
VHL is characterized by hemangioblastomas of the retina and central nervous system (CNS); renal cysts; clear cell carcinoma; pheochromocytomas (PCC); endolymphatic sac tumors; cystadenomas of the epididymis in males and broad ligament of uterus in females; pancreatic cysts, cystadenomas and neuroendocrine tumors (1,2).
An increased frequency of pancreatic neuroendocrine tumors, endolymphatic sac tumors, epididymal tumors, and benign cysts in the pancreas and the kidneys is also reported.