References in periodicals archive ?
Although HLH can occur in all age groups, neonatal onset is rare, accounting for only 4% of all HLH cases.
Four months later, (14 months after the initial diagnosis of ALL), the patient was diagnosed with secondary HLH based on the updated Henter's criteria3 including: unexplained fever, chronic pancytopenia (white blood cell count 1.
Inactivation of MyoD in mice leads to up-regulation of the myogenic HLH gene Myf-5 and results in apparently normal muscle development.
Initiation of chemotherapy was planned as per the HLH 2004 protocol,  and a bone-marrow transplant was to be considered; however, the parents did not opt for any escalation of treatment and wanted to continue with the conservative management.
HLH is a life-threatening syndrome of excessive immune activation that results in tissue damage.
Thus, HLH secondary to infection was considered and intravenous immunoglobulin at a dose of 1 g/kg/day was administered for two days.
Only one in about 1 million children are diagnosed with HLH, which makes the disease a hard one to identify and then adequately fight.
Criterios diagnosticos de linfohistiocitosis hemofagocitica  Diagnostico molecular de HLH o la presencia de 5 de 8 de los siguientes criterios: 1.
Many clinical manifestations of PDH overlap with those of the hyperinflammatory condition hemophagocytic lymphohistiocytosis (HLH), and co-existence of HLH and histoplasmosis has been reported in adults.
The diagnosis of HLH was ruled out, as the patient did not manifest some of the main diagnostic criteria such as cytopenia, splenomegaly, hypertriglyceridemia, and hypofibrinogenemia.
Familail Hemophagocytic Lymphohistiocystisis occurs typically in children under 1 year of age, secondary HLH typically occurs after 6 years of age.
The authors attributed HLH in association with leprosy; however, the patient was diagnosed with systemic lupus erythematosus (SLE) 1 year prior to her current presentation.
Acronyms browser ?
Full browser ?
- HLH (Hemophagocytic lymphohistiocytosis)