HSAN IVHereditary Sensory and Autonomic Neuropathy Type IV
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Patients with HSAN IV should be carefully monitored throughout the lifetime by a dental team as soon as the diagnosis is made and the parents should be made conscious about dental treatment needs of their children to maintain the patients' social, psychological and behavioral rehabilitation.
Se han identificado cinco tipos de HSAN, y esta clasificacion se basa en el patron hereditario, las caracteristicas clinicas y los sistemas de neuronas mas afectados: HSAN I, neuropatia hereditaria sensorial radicular; HSAN II, deterioro para la discriminacion de estimulos de tacto y presion; HSAN III, sindrome familiar disautonomico Riley-Day; HSAN IV insensibilidad congenita al dolor con anhidrosis, y HSAN V (3).
Five types of HSAN have been identified, and this classification is based on the hereditary pattern, the clinical features and the most affected neuronal systems: HSAN I, hereditary sensory radicular neuropathy; HSAN II, impairment of the discrimination of tactile and pressure stimuli; HSAN III, familial dysautonomia (Riley-Day Syndrome); HSAN IV congenital insensitivity to pain with anhidrosis, and HSAN V (3).