JEB-PAJunctional Epidermolysis Bullosa with Pyloric Atresia
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As previously mentioned, JEB is further broken down into 3 main categories: JEB Herlitz (JEB-H), JEB non-Herlitz (JEB-nH), and JEB with pyloric atresia (JEB-PA).
There is no definitive treatment for JEB-PA. If a prenatal diagnosis is established, a caesarean section should be considered to reduce trauma during delivery.
In many cases, the course of JEB-PA is relentless and fatal despite surgical correction of concomitant PA.