as primary genitourinary system have been reported rarely in the kidney, bladder, and prostate.
are uncommon entities especially for the female genital tract and the ovaries are the most common location (1-15).
The delayed diagnosis of VHL disease was made after the occurrence of cranial hemangioblastoma in the first case and PNET
in the second case.
Salomao et al., "Small, nonfunctioning, asymptomatic pancreatic neuroendocrine tumors (PNETs
): role for nonoperative management," Surgery, vol.
Insulinomas, unlike other pNET
, are typically benign tumors, and therefore it is possible to speculate that this might be due to particular molecular events.
Diagnosis of tumors was based on the International Classification of Disease for Oncology, third revision (ICD-O-3) histology codes for ES (code 9260) and PNET
This group consists of Ewing sarcoma, PNETs
, rhabdomyosarcoma, synovial sarcoma, non-Hodgkin's lymphoma, retinoblastoma, neuroblastoma, hepatoblastoma, nephroblastoma, small cell osteogenic sarcoma, Wilm's tumor, and desmoplastic small round cell tumor.
Pathology was consistent with mature teratoma (90%) and PNET
Glioblastoma with primitive neuronal component, which has been referred to as glioblastoma with the primitive neuroectodermal tumor-like component (GBM-PNET) in the literature and which is one of the emerging GBM subtypes, is a rare tumor with the combined features of malignant glioma and PNET
. Here, we report a long-term survival patient who presented not only this rare collision tumor but also different histopathological components in the disease course.
We report a case of intracranial Ewing's sarcoma, which was initially suspected to be a central nervous system PNET
(c-PNET) in an 8-year-old girl.
CD99 is atransmembrane glycoprotein encoded by MIC2 gene and is expressed in Ewing's sarcoma, PNET
, acute lymphoblastic lymphoma, leukemia, acute myelogenous leukemia, myeloid sarcoma, synovial sarcoma and mesenchymal chondrosarcoma.
Ross was diagnosed with a rare grade-4 primitive neuroectodermal tumour (PNET
) in 2014 and underwent brain surgery and chemotherapy.